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Your search returned 66 studies. (Get alerts for new studies):Role of Toxins in Lung Infections Caused by Pseudomonas AeruginosaConditions: Pseudomonas Infection - Cystic Fibrosis3 Locations availableBlood Collection From Individuals With Lung Disease for Genetic StudiesConditions: Asthma - COPD - Interstitial Lung Disease - Cystic Fibrosis - Lung Cancer1 Location availableUsing Rheological Methods to Characterize Cystic Fibrosis (CF) Sputum and the Effects of Mucoactive AgentsConditions: Cystic Fibrosis1 Location availableExercise-Induced Bronchospasm in Cystic FibrosisConditions: Cystic Fibrosis - Bronchospasm1 Location availableAerosolized Hypertonic Xylitol Versus Hypertonic Saline in Cystic Fibrosis (CF) SubjectsConditions: Cystic Fibrosis1 Location availableMicrobial Community Composition and Metabolism in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableDifferentiating Outcome Measures in Infants/Young Children With Cystic Fibrosis Utilizing Controlled Ventilation Infant/Young Child Chest CT Scanning Conditions: Cystic Fibrosis1 Location availableOpen-label Vitamin D Trial for Patients With Cystic Fibrosis and Allergic Bronchopulmonary AspergillosisConditions: Cystic Fibrosis - Allergic Bronchopulmonary Aspergillosis - A. Fumigatus2 Locations availablePhase 2 Study of Ex-vivo Perfusion and Ventilation of Lungs to Assess Transplant SuitabilityConditions: Emphysema - Chronic Obstructive Pulmonary Disease (COPD) - Cystic Fibrosis - Pulmonary Fibrosis - Bronchiectasis - Sarcoidosis - Pulmonary Hypertension - Alpha-1 Antitrypsin Deficiency2 Locations availableHyperpolarized 129Xe MRI for Imaging Pulmonary FunctionConditions: Asthma - Chronic Obstructive Pulmonary Disease - Interstitial Lung Disease - Cystic Fibrosis - Pulmonary Hypertension1 Location availableStudying Patients With Cystic Fibrosis and Other Pulmonary and Pancreatic DisordersConditions: Bronchiectasis - Cystic Fibrosis - Pancreatic Insufficiency1 Location availableThe Role of Bacteria and Genetic Variations in Cystic FibrosisConditions: Lung Diseases4 Locations availableEvaluation of Autosomal Recessive Polycystic Kidney Disease and Congenital Hepatic FibrosisConditions: Autosomal Recessive Polycystic Kidney Disease - Congenital Hepatic Fibrosis - Caroli's Disease - Polycystic Kidney Disease - Joubert Syndrome - Cerebro-Oculo-Renal Syndromes - COACH Syndrome - Senior-Loken Syndrome - Dekaban-Arima Syndrome - Cogan Oculomo1 Location availableMechanisms of Immune Tolerance and Inflammation in Patients With Cystic Fibrosis With ABPAConditions: Cystic Fibrosis - Allergic Bronchopulmonary Aspergillosis1 Location availableUse of Levemir® Improves Metabolic and Clinical Status in Cystic Fibrosis-related Diabetes (CFRD)Conditions: Cystic Fibrosis Related Diabetes1 Location availableSafety and Efficacy of Sildenafil in Cystic Fibrosis (CF) Lung DiseaseConditions: Cystic Fibrosis1 Location availableTransfer Impedance in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableEarly Methicillin-resistant Staphylococcus Aureus (MRSA) Therapy in Cystic Fibrosis (CF)Conditions: Cystic Fibrosis - Methicillin-resistant Staphylococcus Aureus9 Locations availableInhaled Xylitol Versus Saline in Stable Subjects With Cystic FibrosisConditions: Cystic Fibrosis2 Locations availableImaging Airway Liquid Absorption in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableClinical Evaluation of NeoPlex4 Assay and NeoPlex SystemConditions: Adrenal Hyperplasia, Congenital - Congenital Hypothyroidism - Cystic Fibrosis3 Locations availableTissue Bank for Pulmonary DiseasesConditions: Cystic Fibrosis1 Location availableIGF-1 Therapy in Patients With Cystic FibrosisConditions: Cystic Fibrosis2 Locations availableNatural History of BronchiectasisConditions: Bronchiectasis - Cystic Fibrosis - Autoimmune Disease - Common Variable Immunodeficiency1 Location availableGenetic Modifiers of Cystic Fibrosis Related DiabetesConditions: Cystic Fibrosis Related Diabetes1 Location availableStudy of Yoga as a Therapy for Cystic Fibrosis (CF) PatientsConditions: Cystic Fibrosis1 Location availableUAB HRFD Core Center: Core A: The Hepato/Renal Fibrocystic Diseases Translational ResourceConditions: Hepato/Renal Fibrocystic Disease - Autosomal Recessive Polycystic Kidney Disease - Joubert Syndrome - Bardet Biedl Syndrome - Meckel-Gruber Syndrome - Congenital Hepatic Fibrosis - Caroli Syndrome - Oro-Facial-Digital Syndrome Type I - Nephronophithisis -1 Location availablePharmacokinetics of Vancomycin for Inhalation in Cystic FibrosisConditions: Cystic Fibrosis - Methicillin-resistant Staphylococcus Aureus1 Location availableGene Modifiers of Cystic Fibrosis Lung DiseaseConditions: Cystic Fibrosis - Lung Diseases1 Location availableExercise Training Study for Patients With Cystic FibrosisConditions: Cystic Fibrosis - Self Regulated Exercise1 Location availablePhase II Study of Digitoxin to Treat Cystic FibrosisConditions: Cystic Fibrosis1 Location availableGrowth Hormone Therapy for Wasting in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableFDG-PET Imaging in Young Cystic Fibrosis PatientsConditions: Cystic Fibrosis1 Location availablePrevention of Cystic Fibrosis DiabetesConditions: Cystic Fibrosis - Prediabetes3 Locations availableBuilding Adherence to Live With And Navigate my Cystic Fibrosis (CF) ExperienceConditions: Cystic Fibrosis1 Location availablePrediction by Ultrasound of the Risk of Hepatic Cirrhosis in Cystic FibrosisConditions: Cystic Fibrosis - Pancreatic Insufficiency8 Locations availableStudy of the Effect of VX-770 on Hyperpolarized Helium-3 Magnetic Resonance Imaging in Subjects With Cystic Fibrosis and the G551D MutationConditions: Cystic Fibrosis1 Location availableI Change Adherence & Raise ExpectationsConditions: Cystic Fibrosis19 Locations availableRare Genetic Disorders of the Breathing AirwaysConditions: Kartagener Syndrome - Cystic Fibrosis - Pseudohypoaldosteronism - Primary Ciliary Dyskinesia7 Locations availableInvestigating Mucinase Activity in Airway DiseaseConditions: Asthma - Cystic Fibrosis - Smokers1 Location availableCFF Biomarkers of ExacerbationConditions: Cystic Fibrosis5 Locations availableOral Docosahexanoic Acid Supplementation in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableEffect of Hypertonic Saline on Mucus Clearance in Children Ages 5-12 With Cystic FibrosisConditions: Cystic Fibrosis - Mucociliary Clearance1 Location availableCostimulatory Molecules as Biomarkers in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableAztreonam Lysine for Pseudomonas Infection Eradication StudyConditions: Cystic Fibrosis26 Locations availableSafety of AZLI in Children With Cystic Fibrosis (CF) and Chronic Pseudomonas Aeruginosa in the Lower AirwaysConditions: Cystic Fibrosis - Pseudomonas Aeruginosa9 Locations availableG551D Observational StudyConditions: Cystic Fibrosis29 Locations availableStudy of VX-661 Alone and in Combination With VX-770 in Subjects Homozygous to the F508del-CFTR MutationConditions: Cystic Fibrosis12 Locations availableNasal Potential Difference (NPD) for the Diagnosis of Cystic FibrosisConditions: Cystic Fibrosis1 Location availableGenetic Modifiers of Cystic Fibrosis (CF) Liver DiseaseConditions: Cystic Fibrosis - Liver Disease1 Location availableStructure and Function of Salivary ProteinsConditions: Cystic Fibrosis1 Location availableEarly Intervention in Cystic Fibrosis ExacerbationConditions: Cystic Fibrosis3 Locations availableBone Microarchitecture at the Radius: a Pilot Comparison Between Children With Cystic Fibrosis and Healthy ControlsConditions: Cystic Fibrosis1 Location availableA Study of Sweat Testing Using a Quantitative PatchConditions: Cystic Fibrosis1 Location availableBaby Observational and Nutritional StudyConditions: Cystic Fibrosis - Growth Failure22 Locations availablePopulation Pharmacokinetics of Prolonged Infusion Meropenem in Cystic Fibrosis (CF) ChildrenConditions: Cystic Fibrosis - Pneumonia - Pseudomonas Aeruginosa Infection3 Locations availableRole of Genetic Factors in the Development of Lung DiseaseConditions: Cystic Fibrosis - Sarcoidosis - Tuberous Sclerosis - Asthma2 Locations availableGenetic Disorders of Mucociliary Clearance in Nontuberculous Mycobacterial Lung DiseaseConditions: Mycobacteria, Atypical - Cystic Fibrosis - Ciliary Disorders - Pseudohypoaldosteronism - Bronchiectasis1 Location availableA Pharmacokinetic and Safety Study of IV Gallium Nitrate (Ganite) in Cystic Fibrosis PatientsConditions: Cystic Fibrosis2 Locations availableTrial of Doxycycline to Reduce Sputum MMP-9 Activity in Adult Cystic Fibrosis (CF) PatientsConditions: Cystic Fibrosis1 Location availableMolecular Phenotypes for Cystic Fibrosis Lung DiseaseConditions: Cystic Fibrosis - Lung Diseases1 Location availableAbsorptive Clearance After Inhaled Osmotics in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableStudy of Mycobacterial InfectionsConditions: Atypical Mycobacterium Infections - Cystic Fibrosis - Job's Syndrome1 Location availableConcurrent Single Gene and 24 Chromosome Aneuploidy Preimplantation Genetic Diagnosis (PGD)Conditions: Any Single Gene Disorder (Cystic Fibrosis, Tay-Sachs)1 Location availableDurability of Hypertonic Saline for Enhancing Mucociliary Clearance in Cystic FibrosisConditions: Cystic Fibrosis1 Location availableProspective Observational Study to Evaluate Biomarkers of Aminoglycoside Nephrotoxicity in Patients With Cystic FibrosisConditions: Cystic Fibrosis2 Locations available
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